Hyderabad: A complex liver transplant performed by the Surgeons at Kamineni Hospitals, LB Nagar, Hyderabad, brought a new life to a 29-year-old fitness enthusiast and Mr. Delhi contestant, who suffered from a rare genetic disorder called Biliary Atresia (deficiency/absence of bile duct from birth).
Ayush Garg, from East Delhi, was admitted to the hospital with a rare genetic disorder i.e. Biliary Atresia. This rare genetic disorder occurs in 1:1,000 people. The patient underwent surgery at the age of 2 months – Kasai procedure (Hepatico-Porto-enterostomy). This procedure failed after 15 years leading to fleeting jaundice, intractable Itching, fever, loss of appetite, and significant loss of weight. He had undergone repeated interventional procedures which all proved futile.
“Complications seen in this rare disorder are recurrent episodes of cholangitis, requiring technically challenging surgery because of previous biliary surgery and multiple biliary interventions (PTBD extensive vascular adhesions, severe portal hypertension).
Children with biliary atresia may have reduced bile flow to the small intestine, coupled with liver damage, which may lead to malnutrition. To make sure infants and children with biliary atresia get enough nutrients and calories, we recommend a special diet plan and supplements,” – Dr. Rajasekhar Perumalla, Director – Hepatobiliary & Transplant Surgery, Kamineni Hospitals, Hyderabad.